ENFISEMA LOBAR CONGENITO PDF

Download PDF. 1 / 2 Pages. Previous article. Go back to website. Next article. Download scientific diagram | – (Caso 4) Suspeita de en fi sema lobar congénito no lobo superior direito from publication: Enfisema lobar congénito com. Request PDF on ResearchGate | Enfisema lobar congénito: Presentación de 4 casos | SUMMARY Congenital lobar emphysema is an unfrequent congenital.

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For all other comments, please send lobr remarks via contact us. Only comments written in English can be processed. Congenital lobar emphysema CLE is a respiratory abnormality characterized by respiratory distress due to hyperinflation of one or more affected lobes of the lung. Most cases present in the neonatal period or in early infancy. Patients with less severe manifestations may present in early childhood or rarely in adulthood.

ENFISEMA LOBAR CONGENITO EPUB DOWNLOAD

encisema Clinical picture can range from asymptomatic or mildly symptomatic to severe respiratory impairment requiring immediate intervention. Symptomatic patients present with respiratory distress, dyspnea, tachycardia, cyanosis, and failure to thrive.

Polyalveolar lobe has also been reported as a cause of CLE. Chest X ray and CT scan are the key imaging modalities used for diagnosis.

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Chest X ray shows hyperlucent affected lobes with mediastinal shift and collapse of ipsilateral unaffected segments.

CT scan provides details of affected lobes and vascular involvement.

ENFISEMA LOBAR CONGENITO EPUB DOWNLOAD

Echocardiography to detect concomitant heart disease can also be performed. Respiratory distress and radiolucency in chest X rays can lead to lobad misdiagnosis of tension pneumothorax.

Differential diagnoses also include congenital pulmonary airway malformation see this termpneumonia, bronchiolitis and foreign body aspiration. Prenatal diagnosis can be made with ultrasonography by identifying hyperechoic areas in fetal lung.

Lobectomy of affected lobes is the widely accepted form of management with a satisfactory outcome. Asymptomatic or mildly symptomatic cases can be managed conservatively but follow up is necessary. Thoracoscopic resection has been attempted and seems to have better post operative outcomes.

Asymptomatic cases may regress spontaneously. Prompt diagnosis and surgical intervention usually provide good long term outcome in symptomatic cases. In some cases, CLE can be lethal. Other search option s Alphabetical list.

Orphanet: Enfisema lobar congenito

Summary and related texts. Check this box if you wish to receive a copy of your message. Disease definition Congenital lobar emphysema CLE is a respiratory abnormality characterized by respiratory distress due to hyperinflation of one or more affected lobes of the lung. Congenital lobar conenito Infantile lobar hyperinflation Prevalence: Clinical description Most cases present in the neonatal period or in early infancy.

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Diagnostic methods Chest X ray and CT scan are the key imaging modalities used for diagnosis. Differential diagnosis Respiratory distress and radiolucency in chest X rays can lead to a misdiagnosis of tension pneumothorax. Antenatal diagnosis Prenatal diagnosis can be made with ultrasonography by identifying hyperechoic areas in fetal lung.

Management and treatment Lobectomy of affected lobes is the widely accepted form of management with a satisfactory outcome. Prognosis Asymptomatic cases may regress spontaneously. Detailed information Professionals Summary information Suomipdf Russianpdf Clinical practice guidelines Deutsch Health care resources for this disease Expert centres 72 Diagnostic tests 0 Patient organisations 18 Orphan drug s 0.

Specialised Social Services Eurordis directory. The documents contained in this web site are presented for information purposes only. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment.